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abortion, spontaneous
acetylcholine receptor
acetylcholine receptor antibody
advances in neurology
adverse drug reaction
agenesis of corpus callosum
Aicardi's syndrome
alpha-fetoprotein
Alzheimer's disease
amniocentesis
amyotrophic lateral sclerosis
amyotrophic lateral sclerosis, epidemiology of
amyotrophic lateral sclerosis, familial
amyotrophic lateral sclerosis, guamian type of
ANA
anesthesia, general
anesthesia, local
anti basal ganglia antibodies
anti MAG antibodies
antimetabolite
antistreptolysin titer
antithyroid antibodies
aphasia
areflexia
arthrogryposis multiplex
asymptomatic
ataxia
ataxia, truncal
atidarsagene autotemcel
autism
autoantibodies
autoimmune disease
axonal spheroid
azathioprine
Babinski sign
basal ganglia
basal ganglia, lesion of
basal ganglia, lesion, bilateral
bilateral periventricular nodular heterotopia
brain atrophy
brain biopsy
breast feeding
burst suppression pattern, electroencephalogram
CAT scan, abnormal
catatonia
central core disease
cerebellar degeneration
cerebral cortex
cerebrospinal fluid, elevated protein of
cerebrospinal fluid, lactic acid concentration
cesarean section
Charcot-Marie-Tooth
cherry red spot
cherry red spot-myoclonus syndrome
children
chorioretinitis
chromosomal abnormality
chromosome 5
Clinical Pathologic Conference(C.P.C.)
coloboma
complications
confusion
confusional state, acute
congenital malformation
congenital malformation, non CNS
congenital myasthenic syndromes
corpus callosum
cortical dysplasia, focal
cyst, porencephalic
deep gray nuclei
degenerative diseases of CNS
dentate nuclei
dentate nuclei, lesion of
developmental milestones
developmental milestones, loss of
developmental retardation
differential diagnosis
drooling
dropped head syndrome
drug induced neurologic disorders
dyskinesia
dysphagia
dystonia
efficacy
electroencephalogram
electroencephalogram, abnormalities of
emotional lability
encephalitis
encephalitis, autoimmune
encephalitis, focal
encephalitis, Rasmussen's
encephalomyelitis, postinfectious
encephalopathy
encephalopathy, Hashimoto's
enzyme, defect
epidemiology of neurology
epilepsia partialis continua
eye movement, disorders of
Fabry's disease
facial asymmetry
falling
familial
Fazio-Londe's disease
fever
FLAMES
floppy infant
Friedreich's ataxia
gammaglobulin therapy, intravenous
gangliosidosis GM2
gaze palsy
gaze palsy, supranuclear
gene
gene therapy
genetic neurologic disorders
genetic screening
hallucination
headache
heavy metal intoxication
hemihypertrophy, congenital
hemiparesis
hemispherectomy
hepatomegaly
heterotopia
hexosaminidase-A
hexosaminidase-A and B
histopathology
Huntington's chorea
hyperreflexia
hypomelanosis of Ito
hypomyelination
hypopigmentation of skin
hypotonia
hypotonia, infants
immunologic disease
immunosuppressive agents
inborn errors of metabolism
inclusion bodies
inclusion bodies, eosinophilic cytoplasmic
infantile bilateral striatal necrosis
infantile neuronal degeneration
infantile spasm
insomnia
intellectual deficit
intellectual deterioration
iron, brain
Jewish
Kugelberg-Welander syndrome
labor, complicated
lactic acidemia
Leigh's disease
lethargy
leukodystrophy
level of consciousness, decreased
lipid storage disorder of CNS
lysosomal storage disease
macrocephaly
magnesium sulfate
malabsorption
malformation, CNS, congenital
Mary Walker phenomenon
megalencephaly
meningeal enhancement
mental retardation
mental status, abnormal
mesial temporal sclerosis
metachromatic leukodystrophy
metachromatic leukodystrophy, juvenile
metachromatic leukodystrophy, late-infantile
microcephaly
micropthalmia
misdiagnosis
molecular genetics
monoclonal antibodies
mortality
motor neuron disease
MRI
MRI, abnormal
MRI, CAT scan compared to
MRI, contrast enhanced
MRI, cortical enhancement
MRI, diffusion weighted
MRI, eye of tiger sign
MRI, gradient-echo
MRI, hypointense signal foci on
MRI, negative
MRI, paramagnetic effect
muscle biopsy
muscle spasm
muscle wasting, diffuse
muscular dystrophy, Duchenne
mutism
myasthenia gravis
myasthenia gravis, classification
myasthenia gravis, congenital
myasthenia gravis, infantile and juvenile
myasthenia gravis, neonatal
myasthenia gravis, neuromuscular junction in
myasthenia gravis, passive transfer of
myasthenia gravis, receptor site in
myasthenia gravis, seronegative
myasthenia gravis, thymectomy in
myasthenia gravis, treatment of
myasthenic crisis
myoclonus
myoclonus, epilepsy
myopathy
myopathy, metabolic
myotonia dystrophica
neoplasm, peripheral nerve
neoplasm, primary of CNS
neoplasm, primary of CNS-children
nerve conduction studies
nerve conduction studies, motor
neuroaxonal dystrophy
neuroaxonal dystrophy, infantile
neurocutaneous disease
neurofibrillary degeneration
neurologic disease, diagnoses of
neurologic examination, focal
neuronal cell death
neuronal ceroid-lipofuscinosis
neuronal degeneration
neuronal migration disorder
neuroophthalmology
neuropathology
neuropathology, brain
neuropathy
night sweats
NMDA antagonists
nystagmus
nystagmus, rotary
opisthotonus
optic atrophy
optic nerve
optic nerve, lesion of
optic neuritis
PANK2 mutation
paraparesis, familial spastic
Parkinson disease
paroxysmal neurologic disorder
patient information and support
pediatric neurology
perineural invasion
personality change
plasmapheresis
pleocytosis of cerebrospinal fluid
pleocytosis of cerebrospinal fluid, neutrophilic
poison, mercury
poison, neurologic problems with
Pompe's disease of glycogen storage
Pompe's disease, infantile
postural abnormality
pregnancy, neurologic complications in
prenatal diagnosis by amniocentesis
prognosis
psychiatric problems in neurologic disorders
psychomotor retardation
psychosis, childhood
pyramidal tract dysfunction
pyruvate metabolism, abnormality of
quadriparesis
recurrent
respiratory depression
respiratory failure
respiratory tract infection
retinal degeneration
retropulsion
review article
rigidity
rituximab
safety
Sandhoff's disease
segmental demyelination
seizure
seizure, adult onset
seizure, children
seizure, focal
seizure, intractable
seizure, intractable, treatment of
seizure, neonatal
seizure, prognosis in childhood
seizure, psychomotor-temporal lobe
seizure, surgical treatment of
seizure, treatment of
serologic testing
serologic testing, false negative
seronegative
skin, biopsy
skin, lesions in neurologic disorders
SMN1 gene
sore throat
spasticity
speech disorder
speech disorder, childhood
speech, loss of
spinal cord
spinal cord degeneration
spinal muscular atrophy
spinal muscular atrophy, adult onset
spinal muscular atrophy, classification
spinal muscular atrophy, intermediate form
spinocerebellar ataxia
startle reaction
status epilepticus
steroid
steroid therapy, CNS treatment and complications with
stillbirth
storage disease of CNS
streptococcal infection
striatal encephalitis
striatonigral degeneration
striatonigral degeneration, infantile
striatum, lesion of
Sturge-Weber syndrome
subacute sclerosing panencephalitis(S.S.P.E.)Dawson's disease
survival motor neuron gene
symmetric brain lesions
systemic lupus erythematosus
systemic lupus erythematosus, neonatal
systemic lupus erythematosus, neurologic complications with
Tay-Sachs disease
temporal lobe, status
thalamus, lesion of
thalamus, lesion of-bilateral
thymectomy
thymus and neuromuscular function
thyroiditis
titubation
tone, muscle, increased
treatment of neurologic disorder
tremor
tremor, intention
tricresylphosphate
trinucleotide repeats
tuberous sclerosis
ventricular enlargement
visual acuity, decreased
visual fields, constricted
visual loss
weakness
weakness, generalized
Werdnig-Hoffman disease
West disease
white matter disease
wide based gait
Showing articles 300 to 350 of 1511 << Previous Next >>

Cavernous Sinus Thrombosis in Children
Stroke 46:2657-2660, Press, C.A.,et al, 2015

Autoimmune Post-Herpes Simplex Encephalitis of Adults and Teenagers
Neurol 85:1736-1743, 1730, Armangue, T.,et al, 2015

Recognizing Autoimmune-Mediated Encephalitis in the Differential Diagnosis of Limbic Disorders
AJNR 36:2196-2205, da Rocha, A.J.,et al, 2015

Molybdenum Cofactor Deficiency
Neurol 85:e175-e178, Nagappa, M.,et al, 2015

Community Based Case-Control Study of Childhood Stroke Risk Associated with Congenital Heart Disease
Stroke 46:336-340, Fox, C.K.,et al, 2015

Acute Ischemic Stroke in Pediatric Patients
Stroke 46:e32-e33, Mittal, S.O.,et al, 2015

Multiple-System Atrophy
NEJM 372:249-263, Fanciulli, A. & Wenning, G.K., 2015

Short Myelitis Lesions in Aquaporin-4-IgG-Positive Neuromyelitis Optica Spectrum Disorders
JAMA Neurol 72:81-87, Flanagan, E.P.,et al, 2015

Clinicopathologic Conference, Frontotemporal Lobar Degeneration with Tau-positive Inclusions (Picks Disease Subtype) Due to a Gly389Arg MAPT Mutation, Resulting in the Behavioral Variant of Frontotemporal Dementia with Parkinsonism
NEJM 372:1151-1162, Miller, B.L.,et al, 2015

Anti-Mog Antibodies with Longitudinally Extensive Transverse Myelitis Preceded by Clippers
Neurol 84:1177-1179, Symmonds, M.,et al, 2015

Two Cases of Congenital Myasthenic Syndrome with Vocal Cord Paralysis
Neurol 84:1281-1282, Al-Shahoumi, R.,et al, 2015

Tonic Eye Deviation in Stiff-Person Syndrome
Neurol 84:e124-e127, Chakravarthi, S.,et al, 2015

Inflammatory Muscle Diseases
NEJM 372:1734-1747, Dalakas, M.C., 2015

Clinicopathologic Conference, CAT Scratch Disease (Encephalopathy Associated with Bartonella Henselae)
NEJM 372:2050-2058, Case 16-2015, 2015

Encephalitis and AMPA Receptor Antibodies
Neurol 84:2403-2412, Hoftberger, R.,et al, 2015

Paraneoplastic Neurologic Disorders in Small Cell Lung Carcinoma
Neurol 85:235-239, Gozzard, P.,et al, 2015

Dystonia in Children and Adolescents: A Systematic Review and a New Diagnostic Algorithm
JNNP 86:774-781, Van Egmond, M.E.,et al, 2015

Paraneoplastic Neurological Syndromes and Glutamic Acid Decarboxylase Antibodies
JAMA Neurol 72:874-881,861, Arino, H.,et al, 2015

Anti-DPPX Encephalitis,Pathogenic Effects of Antibodies on Gut and Brain Neurons
Neurol 85:890-897, Piepgras,J.,et al, 2015

Recurrent Stroke in Childhood Cancer Survivors
Neurol 85:1056-1064, Fullerton, H.J.,et al, 2015

Clinical Utility of Acetylcholine Receptor Antibody Testing in Ocular Myasthenia Gravis
JAMA Neurol 72:1170-1174, Peeler, C.E.,et al, 2015

Clinical Spectrum of Encephalitis Associated with Antibodies Againts the a-Amino-3-Hydroxy-5-Methyl-4-Isoxazoleproprionic Acid Receptor
JAMA Neurol 72:1163-1169, Joubert, B.,et al, 2015

Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Encephalitis Lethargica (non Economo Disease, sleeping sickness)
Adams & Victors Principles of Neurology, Chp 33, pg 768, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Pyridoxine Dependent Seizures
Adams & Victors Principles of Neurology, Chp 37, pg 951, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Biopterine Deficiency
Adams & Victors Principles of Neurology, Chp 37, pg 951, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Inherited Hypeammonemia
Adams & Victors Principles of Neurology, Chp 37, pg 952, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Tay Sachs Disease
Adams & Victors Principles of Neurology, Chp 37, pg 957, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Lipogranulomatosis (Farber Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 960, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Metachromatic Leukodystrophy
Adams & Victors Principles of Neurology, Chp 37, pg 971, Ropper, A.H.,et al, 2014

Inherited Metabolic Diseases of the Nervous System, Neuronal Ceroid Lipofuscinosis (Batten Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 973, Ropper, A.H.,et al, 2014

Brugada Syndrome in Spinal and Bulbar Muscular Atrophy
Neurol 82:1813-1821, Araki, A.,et al, 2014

Pathognomonic Seizures in Limbic Encephalitis Associated with Anti-LGl1 antibodies
Lancet 383:2018, Sen, A.,et al, 2014

A 72-year-old Man with Rapid Cognitive Decline and Unilateral Muscle Jerks
Neurol 82:e194-e197, Duncan, M.,et al, 2014

Effect of Rituximab in Patients with Leucine-Rich, Glioma-Inactivated 1 Antibody-Associated Encephalopathy
JAMA Neurol 71:896-900, Irani, S.R.,et al, 2014

Somatic Mutations in Cerebral Cortical Malformations
NEJM 371:733-743, Jamuar, S.S.,et al, 2014

Controlled Trial of Transfusions for Silent Cerebral Infarcts in Sickle Cell Anemia
NEJM 371:699-710, DeBaun, M.R.,et al, 2014

Progressive Cerebellar Ataxia and New-Onset Diabetes
Lancet 383:186, Kong, M.,et al, 2014

Limbic Encephalitis Associated with Anti-Voltage-Gated Potassium Channel Complex Antibodies Mimicking Creutzfeldt-Jakob Disease
JAMA Neurol 71:79-82, Yoo,J.Y. & Hirsch, L.J., 2014

Neuronal Intranuclear Inclusion Disease Cases with Leukoencephalopathy Diagnosed via Skin Biopsy
JNNP 85:354-356, Sone, J.,et al, 2014

Stiff Person Syndrome Masquerading as Panic Attacks
Lancet 383:668, Ho, C.S.H.,et al, 2014

Clinical Specificities of Adult Male Patients with NMDA Receptor Antibodies Encephalitis
Neurol 82:556-563, Viaccoz, A.,et al, 2014

Transient Ischemic Attack Requiring Hospitalization of Children in the United States
Stroke 45:887-888, Adil, M.M.,et al, 2014

Drug Treatment of Epilepsy in Adults
BMJ 348:g2546, Schmidt, D. & Schachter, S.C., 2014

Early-Onset Stroke and Vasculopathy Associated with Mutations in ADA2
NEJM 370:911-920, Zhou, Q.,et al, 2014

Autism
Lancet 383:896-910, Lai, M.C.,et al, 2014

Herpes Simplex Encephalitis as a Potential Cause of Anti-N-Methyl-D-Aspartate Receptor Antibody Encephalitis
JAMA Neurol 71:344-346, DeSena, A.,et al, 2014

Herpes Simplex Virus Encephalitis is a Trigger of Brain Autoimmunity
Ann Neurol 75:317-323, Armangue, T.,et al, 2014

Stroke and NonStroke Brain Attacks in Children
Neurol 82:1434-1440, Mackay, M.T.,et al, 2014

Myasthenia in Pregnancy: Best Practice Guidelines from a UK Multispecialty Working Group
JNNP 85:538-543, Norwood, F.,et al, 2014

Utility of an Immunotherapy Trial in Evaluating Patients with Presumed Autoimmune Epilepsy
Neurol 82:1578-1586, Toledano, M.,et al, 2014



Showing articles 300 to 350 of 1511 << Previous Next >>