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Differential
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abdominal distention
abdominal muscle paralysis
abdominal protrusion
acid maltase deficiency
acid maltase deficiency, adult
acquired immunodeficiency syndrome
adverse drug reaction
alcohol
alcohol, heart involvement with
alcohol, neurologic complications with
alcoholism
alpha glucosidase
amyloid
amyloidosis
amyotrophic lateral sclerosis
amyotrophic lateral sclerosis, bulbar
amyotrophic lateral sclerosis, atypical
amyotrophic lateral sclerosis, differential diagnosis
amyotrophic lateral sclerosis, familial
amyotrophic lateral sclerosis, misdiagnosis
amyotrophic lateral sclerosis, prognosis
ankle reflex, preserved
anterior horn cell disease
anti signal recognition particle antibody
aphonia
areflexia
arm weakness
arrhythmia, cardiac
arthralgia
arthrogryposis multiplex
aspartate aminotransferase
asymptomatic
ataxia
ataxia, sensory
ataxic gait
atrioventricular block
autoantibodies
autoimmune disease
azidodeoxythymidine
bone biopsy
bone pain
bone scanning
brachial neuritis
brachial neuritis, acute
brachial neuritis, bilateral
brachial plexus neuropathy
brachial plexus neuropathy, bilateral
brachial plexus neuropathy, children
brachial plexus neuropathy, familial
brachial plexus neuropathy, recurrent
bradycardia
bulbar palsy
burning feet
burning paresthesia
cachexia
CAG repeats
calcification, intracranial
calf atrophy
calf hypertrophy
carcinoma
cardiomegaly
cardiomyopathy
cardiovascular disease
carpal tunnel syndrome
case studies
CAT scan
CAT scan, abnormal
CAT scan, false negative
central core disease
cerebellar atrophy, secondary
cerebellar degeneration
cerebellar edema
cerebellar lesion
cerebral cortical atrophy
cerebral edema
cerebral embolism
cerebrospinal fluid, elevated protein of
cerebrospinal fluid, eosinophilia of
cerebrospinal fluid, lactic acid concentration
cerebrovascular accident
cerebrovascular accident, multiple
cerebrovascular accident, young adult
Charcot-Marie-Tooth
chewing, impaired
children
chromosomal abnormality
chromosome 5
chronic progressive external ophthalmoplegia
Clinical Pathologic Conference(C.P.C.)
clubfoot as related to neurologic disease
cold temperature
coma
conduction block
congenital heart disease
congestive heart failure
consanguinity
contractures, joint
creatine phosphokinase(CPK)elevated
cultured skin fibroblasts
deafness
delay in diagnosis
dementia
dementia, frontotemporal
dermatomyositis
developmental milestones
developmental retardation
diabetes mellitus
diabetes mellitus, neurologic manifestations of
diabetic amyotrophy
diarrhea
differential diagnosis
difficulty climbing stairs
diplopia
dislocated hip, congenital
distal muscle atrophy
distal muscle weakness
drug induced neurologic disorders
dysarthria
DYSF gene
dysferlin
dysferlinopathy
dysmorphic
dysphagia
dysphonia
dyspnea
dyspraxia
dystrophic calcification
dystrophin
echocardiogram
electrocardiogram, abnormal
electromyogram
electromyogram, decremental response
electron microscopy
Emery-Dreifuss muscular dystrophy
encephalomyelitis
encephalomyelitis, parainfectious
encephalopathy
encephalopathy, progressive
entrapment neuropathy
enzyme treatment
enzyme, defect
enzyme, muscle disease
epidemiology of neurology
exercise
extraocular muscle lesion
facial weakness
facial weakness, bilateral
falling
familial
fasciculation
fatigable chewing
fatigue
fever
fibrillations
finger flexor weakness
finger weakness
flu-like illness
foot drop
gait disorder
gait, waddling
gammaglobulin therapy, intravenous
gastrocnemius muscle weakness
gastrointestinal disease, neurologic complications
gastrointestinal motility
gastroparesis
gender
gene
gene mutation
gene therapy
genetic counselling
genetic neurologic disorders
genetic screening
genetic testing
glycogen debranching enzyme deficiency
glycogen storage disease
gray matter
Guillain Barre syndrome
Guillain Barre syndrome, differential diagnosis of
gynecomastia
hallucination
hand weakness
headache
headache, severe
headache, worst of life
hearing loss
heart block
heart block, complete
heart murmur
hepatomegaly
heralding manifestation
hip flexor weakness
histochemistry of muscle
hoarseness
Hoesch test
human immunodeficiency virus type 1
hypercalcemia
hyperparathyroidism
hyperreflexia
hypertension
hyperthyroidism
hypoglycemia
hyponatremia
hypophonia
hyporeflexia
hypotelorism
hypotonia
hypotonia, infants
immediate recall
immunosuppressive agents
inability to stand on tiptoes
inclusion bodies
inclusion bodies, eosinophilic intranuclear
inclusion body myositis
intestinal pseudoobstruction
intrinsic hand muscles, wasting of
klippel feil syndrome
Kugelberg-Welander syndrome
kyphoscoliosis, neurologic causes of
lactic acidemia
lead poisoning
leg atrophy
leg numbness
leg weakness, bilateral
leg weakness, unilateral
leukodystrophy
level of consciousness, decreased
lid closure, weakness of
life expectancy
lumbosacral plexopathy
lumbosacral plexus
lumbosacral plexus, neuritis
lymphadenopathy
lymphadenopathy, cervical
lysosomal storage disease
lysosomes, abnoral
malignant hyperpyrexia
McArdle's disease
medulla oblongata, lesion of
MELAS syndrome
meningeal enhancement
meningismus
meningoencephalomyelitis
mental retardation
mental status, abnormal
mimics
misdiagnosis
mitochondrial disease
mitochondrial encephalomyopathy
mitral valve prolapse
MNGIE syndrome
molecular genetics
monoclonal gammopathy
monoclonal gammopathy of uncertain significance
mononeuritis multiplex
mononeuropathy
monoparesis
mortality
motor neuron disease
motor neuron disease, spontaneous recovery
MRI
MRI, abnormal
MRI, muscle
MRI, spinal cord
MRI, spinal cord, increased intramedullary cord signal
multiple myeloma
muscle atrophy, focal
muscle atrophy, progressive
muscle atrophy, static
muscle biopsy
muscle cramp
muscle diseases, characteristics of
muscle pain
muscle phosphorylase deficiency
muscle stiffness
muscle strength, testing
muscle tenderness
muscle wasting, diffuse
muscle weakness
muscle weakness, insidious onset of
muscle weakness, proximal
muscle, metabolic disorders of
muscular dystrophy
muscular dystrophy, Becker
muscular dystrophy, cardiovascular changes with
muscular dystrophy, classification
muscular dystrophy, differential diagnosis of
muscular dystrophy, distal, Miyoshi
muscular dystrophy, Duchenne
muscular dystrophy, facioscapulohumeral
muscular dystrophy, limb-girdle
myasthenia gravis
myasthenia gravis, differential diagnosis
myasthenia gravis, limb-girdle
myasthenia gravis, misdiagnosis of
myasthenic crisis
mycoplasma
mycoplasma pneumoniae
myocarditis
myoclonus
myoglobinuria
myopathy
myopathy, alcoholic
myopathy, amyloid
myopathy, autoimmune
myopathy, carcinomatous
myopathy, drug-induced
myopathy, hereditary
myopathy, inclusion body
myopathy, inclusion body with Paget's disease
myopathy, mitochondrial
myopathy, necrotizing
myopathy, proximal
myopathy, quadriceps
myopathy, steroid induced
myopathy, thyroid disease causing
myopathy, vacuolar
myositis
myositis, focal
myotonia dystrophica
myotonic discharges
nausea and vomiting
neck stiffness
neck weakness
negative
nemaline rod myopathy
nemaline rod myopathy, adult onset
nerve conduction studies
neuritis, causes of
neuroendocrinology
neurologic complications of, systemic disease
neurologic disease, diagnoses of
neurologic signs
neuroophthalmology
neuropathy
neuropathy, diabetic
neuropathy, hereditary peripheral
neuropathy, motor, multifocal
neuropathy, painful
neuropathy, peripheral
neuropathy, short-fiber
neurotoxin
next-generation sequencing
night sweats
normal
nusinersen
nystagmus
nystagmus, rotary
occupational neurologic disorders
occupational neuropathies
old age, neurology of
ophthalmoplegia
ophthalmoplegia, progressive external
optic atrophy
osteomalacia
pacemaker, cardiac-transvenous
Paget's disease
pain
pain, abdominal
pain, leg
pain, severe
pain, thigh
paralysis
paralysis, use-related
paranoia
paraparesis
paraplegia
paraproteinemia
paraspinal muscle
paraspinal muscle weakness
parathyroid adenoma
paresthesias
photophobia
physical activity
plasma cell dyscrasia
plasmapheresis
pleocytosis of cerebrospinal fluid
poliomyelitis
poliomyelitis, provocation
polymyositis
polyneuropathy
polyneuropathy, chronic inflammatory demyelinating
polyneuropathy, chronic inflammatory demyelinating, variant form
polyneuropathy, chronic inflammatory demyelinating-pure motor syn
polyneuropathy, chronic inflammatory demyelinating-sens atax var
polyneuropathy, chronic inflammatory demyelinating-variant forms
polyradiculoneuropathy
Pompe's disease of glycogen storage
porphyria
positive sharp waves
precipitating factors
pregnancy, neurologic complications in
prenatal diagnosis by amniocentesis
prognosis
progressive neurologic disorder
progressive spinal muscular atrophy
proximal muscle atrophy
pseudohypertrophy
pseudomyotonia
ptosis
puerperium
quadriceps atrophy
quadriceps weakness
rabies, nervous system involvement with
radionuclide imaging, heart
ragged-red fibers
rapidly progressing neurologic illness
rash
recurrent
renal stones
repetitive nerve stimulation
respiratory failure
respiratory tract infection
retina, abnormal
retinal lesion
retrograde axonal flow
review article
rhabdomyolysis
rheumatoid arthritis
sarcoidosis
sclerosis, bone
scoliosis
scoliosis, neurologic association with
screening
seizure
sensorineural hearing loss
sensory symptoms
serologic testing
short stature
shoulder, subluxation
SMN1 gene
spinal cord
spinal cord, lesion of
spinal muscular atrophy
spinal muscular atrophy, adult onset
spinal muscular atrophy, classification
spinal muscular atrophy, intermediate form
standing difficulty
steroid
steroid therapy, CNS treatment and complications with
stiff man syndrome
strokelike episodes
sudden death
survival motor neuron gene
systemic illness
tandem gait, ataxic
temporalis muscle wasting
tetanus
toe walking
tongue, enlarged
tongue, fasciculations of
tongue, weakness
torticollis
toxins, nervous system
transverse smile
treatment of neurologic disorder
trinucleotide repeats
upgaze, paralysis of
upward deviation of eyes
urine, dark
viral infection
viral infection, CNS
walking frame
walking, difficulty with
weakness
weakness, fatiguable
weakness, generalized
weakness, progressive
weakness, proximal
weakness, rapidly progressive
weaning from respirator, failure to
weight loss
Werdnig-Hoffman disease
wheelchair
white matter disease
winging of scapula
X-linked bulbospinal neuronopathy
X-linked myopathy
x-linked myopathy with excessive autophagy
Showing articles 450 to 500 of 4643 << Previous Next >>

Neurogenic Muscle Hypertrophy
Muscle & Nerve 19:811-818996., Gutmann,L., 1996

Palliative Care in Neurology
Neurol 46:870-872, 5981996., Bernat,J.L.,et al, 1996

Is Chronic Respiratory Failure in Neuromuscular Diseases Worth Treating
JNNP 61:1-3, Shneerson,J.M., 1996

Brain and Spinal Cord MRI in Motor Neuron Disease
JNNP 61:314-317, Thorpe,J.W.,et al, 1996

Amyotrophic Lateral Sclerosis and Occupational History
Arch Neurol 53:730-733, Strickland,D.,et al, 1996

Avoiding False Positive Diagnoses of Motor Neuron Disease:Lessons from the Scottish Motor Neuron Disease Register
JNNP 60:147-151, Davenport,R.J.,et al, 1996

Diagnosing Motor Neurone Disease
BMJ 312:650-651, Chancellor,A.M., 1996

Motor Neuron Disease
BMJ 313:244, Shneerson,J.M., 1996

Motor Neuron Disease Presenting as Acute Respiratory Failure:A Clinical and Pathological Study
JNNP 60:455-458, Chen,R.,et al, 1996

Dose-Ranging Study of Riluzole in Amyotrophic Lateral Sclerosis
Lancet 347:1425-1431, Lacomblez,L.,et al, 1996

Skin Involvement in Amyotrophic Lateral Sclerosis
lancet 347:1226-1227, Kolde,G.,et al, 1996

Wolfram Syndrome:Hereditary Diabetes Mellitus with Brainstem and Optic Atrophy
Ann Neurol 39:352-360, Scolding,N.J.,et al, 1996

Campylobacter Jejuni Infection and Anti-GM1 Antibodies in Guillain-Barre Syndrome
Ann Neurol 40:181-187, Jacobs,B.C.,et al, 1996

Pure Motor Hand Weakness
Semin Neurol 16:75-81, Lewis,R.A., 1996

Clinical Heterogeneity of Adhalin Deficiency
Ann Neurol 39:196-202, Morandi,L.,et al, 1996

From Enigmatic to Problematic:The New Molecular Genetics of Childhood Spinal Muscular Atrophy
Neurol 46:335-340, Crawford,T.O., 1996

Autonomic Ganglionitis with Severe Hypertension, Migraine, and Episodic but Fatal Hypotension
Neurol 47:817-821, Lee,H.C.,et al, 1996

Three Get Ready
Arch Neurol 53:1222-1223, Goldblatt,D., 1996

Riluzole
Lancet 348:795-799, Wokke,J., 1996

Atrophy of Bilateral Extraocular Muscles
J Neuro-Ophthalmol 16:286-288, Okamoto,K.,et al, 1996

Erroneous Diagnosis Corrected After 28 Years
Arch Neurol 53:1194-1196, Gordon,P.H.,et al, 1996

Charcot-Marie-Tooth Disease and Related Inherited Neuropathies
Medicine 75:233-250, Murakami,T.,et al, 1996

Motor Neuron Disease, Lymphoproliferative Disease, and Bone Marrow Biopsy
Muscle & Nerve 19:1334-1337996., Louis,E.D.,et al, 1996

Immunoassays Fail to Detect Antibodies Against Neuronal Calcium Channels in Amyotrophic Lateral Sclerosis Serum
Ann Neurol 40:695-700, 6911996., Arsac,C.,et al, 1996

Distal WEakness in Dystrophin-Deficient Muscular Dystrophy
Muscle & Nerve 19:1608-1610996., Felice,K.J., 1996

Motor Neuron Disease with Parkinsonism
Arch Neurol 53:987-991, Qureshi,A.I.,et al, 1996

A Case of Creutzfeldt-Jakob Disease (CJD) Started with Monoparesis of the Left Arm
Rinshi Shinkeigaku 36:1245-1248, Obi, T.,et al, 1996

Late-Onset Mitochondrial Myopathy
Ann Neurol 37:16-23, 31995., Johnston,W.,et al, 1995

Neurologic Aspects of Inflammatory Bowel Disease
Neurol 45:416-421, Lossos,A.,et al, 1995

Lyme Neuroborreliosis
Ann Neurol 37:691-702, Garcia-Monco,J.C.&Benach,J.L., 1995

Myositis:Immunologic Contributions to Understanding Cause, Pathogenesis, and Therapy
Ann Int Med 122:715-724, Plotz,P.H.,et al, 1995

Proximal Myotonic Myopathy Syndrome in the Absence of Trinucleotide Repeat Expansions
Muscle & Nerve 18:782-783995., Stoll,G.,et al, 1995

Mitochondrial DNA and Disease
NEJM 333:638-644, Johns,D.R., 1995

Hypoglycaemia in Spinal Muscular Atrophy
Lancet 346:609-610, Bruce,A.K.,et al, 1995

Genotype-Phenotype Correlation in Adult-Onset Acid Maltase Deficiency
Ann Neurol 38:450-454, Wokke,J.H.J.,et al, 1995

Proximal Myotonic Myopathy, Clin Features of Disorder Similar to Myotonic Dystrophy
Arch Neurol 52:25-31, Ricker,K.,et al, 1995

Clinical and Genetic Studies of Fatal Familial Insomnia
Neurol 45:1068-1075, Reder,A.T.,et al, 1995

Dentatorubral-Pallidoluysian Atrophy:Clin Features Closely Related to Unstable Expansion of Trinucleotide (CAG) Repeat
Ann Neurol 37:769-775, Ikeuchi,T.,et al, 1995

Reflex Sympathetic Dystrophy
BMJ 310:1645-1648, Paice,E., 1995

Reflex Sympathetic Dystrophy in Children
BMJ 310:1648-1649, Lloyd-Thomas,A.R.&Lauder,G., 1995

Encephalopathy with Parkinsonian Features in Children Following Bone Marrow Transplantations and High-Dose Amphotericin B
Ann Neurol 37:810-814, Mott,S.H.,et al, 1995

Adverse Outcomes of Bacterial meningitis in School-Age Survivors
Pediatrics 95:646-655, Grimwood,K.,et al, 1995

Amyotrophic Lateral Sclerosis:Correlation of Clinical & MR Imaging Findings
Radiology 194:263-270, Cheung,G.,et al, 1995

Charcot-Marie-Tooth Neuropathies:From Clinical Description to Molecular Genetics
Muscle & Nerve 18:267-275995., Ionasecu,V.V., 1995

Critical Illness Neuromuscular Disease in Children Manifested as Ventilatory Dependence
J Pediatr 126:259-261, Sheth,R.D.,et al, 1995

Classic Neurogenic Thoracic Outlet Syndrome in a Competitive Swimmer:A True Scalenus Anticus Syndrome
Muscle & Nerve 18:229-233995., Katirji,B.&Hardy,R.W., 1995

Bilateral Ulnar Handcuff Neuropathies with Segmental Conduction Block
Muscle & Nerve 18:1021-1023995., Satkunam,L.&Zochodne,D., 1995

Neurological Multisystem Manifestation in Multiple Symmetric Lipomatosis:A Clinical and Electrophysiological Study
Muscle & Nerve 18:693-698995., Naumann,M.,et al, 1995

Canavan Disease:From Spongy Degeneration to Molecular Analysis
J Pediatr 127:511-517, Matalon,R.,et al, 1995

Clinicopath Conf
Multiple Myeloma with Bilateral Carpal Tunnel Syndrome Probably Due to Secondary Amyloid Deposit, Ca, e38-1995,NEJM 333:1625-1630,1995., 1995



Showing articles 450 to 500 of 4643 << Previous Next >>