Neurodegenerative Diseases and Prions
NEJM 344:1516-1526,1548, Prusiner,S.B., 2001
Amyotrophic Lateral Sclerosis
NEJM 344:1688-1700, Rowland,L.P. & Shneider,N.A., 2001
CSF Detection of the 14-3-3 Protein in Unselected Patients with Dementia
Neurol 56:1528-1533, Burkhard,P.R.,et al, 2001
Stem-Cell Research: Drawing the Line
Lancet 358:163,217, Greenberg,D.S., 2001
Inclusiong Body Myositis Mimicking Motor Neuron Disease
Arch Neurol 58:1253-1256, Dabby,R.,et al, 2001
Recessive Ataxia With Ocular Apraxia
Arch Neurol 58:201-205,173, Barbot,C.,et al, 2001
SCA-12: Tremor with Cerebellar and Cortical Atrophy is Associated with a CAG Repeat Expansion
Neruol 56:299-303,287, O'Hearn,E.,et al, 2001
Headache and CNS White Matter Abnormalities Associated with Gluten Sensitivity
Neurol 56:385-388, Hadjivassiliou,M.,et al, 2001
Genetic Testing in Spinocerebellar Ataxias
Arch Neurol 58:191-195, Tan,E. &Ashizawa,T., 2001
Poliomyelitic-Like Illness in Central European Encephalitis
Neurol 55:299-302, Schellinger,P.D. et al, 2000
Inborn Errors of Metabolism as a Cause of Neurological Disease in Adults: An Approach to Investigation
JNNP 69: 5-12, Gray,R.G.F. et al, 2000
Injections of Botulinum Toxin A Into the Salivary Glands Improve Sialorrhoea in Amyotrophic Lateral Sclerosis
JNNP 69:121-123, Giess,R. et al, 2000
Linkage of Familial Amyotrophic Lateral Sclerosis with Frontotemporal Dementia to Chromosome 9q21-q22
JAMA 284:1664-1669, Hosler,B.A.,et al, 2000
A 44-Year-Old Woman with Difficulty Walking
JAMA 284:2632-2639, Iezzoni,L.I., 2000
Disorders of Upper & Lower Motor Neurons
Neurol in Clin Practice, 3rd Ed., Butterworth, Boston: Ch. 78 p. 2007, Mitasumoto,H., 2000
The Split Hand in ALS has a Cortical Basis
J Neurol Sci 180:66-70, Weber,M.,et al, 2000
Amyotrophic lateral Sclerosis Mimic Syndromes, A Population-Based Study
Arch Neurol 57:109-113, Traynor,B.J.,et al, 2000
Botulinum Toxin is a Useful Treatment in Excessive Drooling of Saliva
JNNP 67:697, Bhatia,K.P.,et al, 1999
A New Metabolite Contributing to N-Acetyl Signal in 1H MRS of the Brain in Salla Disease
Neurol 52:1668-1672, Varho,T.,et al, 1999
Atypical Form of Amyotrophic Lateral Sclerosis
JNNP 66:581-585, Sasaki,S.&Iwata,M., 1999
Practice Parameter:The Care of the Patient with Amyotrophic Lateral Sclerosis (An Evidence-Based Review), Report of the Quality Standards Subcommittee of the AAN
Neurol 52:1311-1323, Miller,R.G.,et al, 1999
Clinicopath Conf:Lymphoplasmocytic Lymphoma with Motor Neuronopathy,Waldenstrom's Macroglobulinemia
NEJM 340:1661-1669, , 1999
Molecular Basis of the Neurodegenerative Disorders
NEJM 340:1970-1980, Martin,J.B., 1999
A Prospecitve Study of Preferences and Actual Treatment Choices in ALS
Neurol 53:278-283,248, Albert,S.M.,et al, 1999
Adult-Onset Nemaline Myopathy:Another Cause of Dropped Head
Muscle & Nerve 22:1146-1150, Lomen-Hoerth,C.,et al, 1999
Pathologic Heterogeneity in Clinically Diagnosed Corticobasal Degeneration
Neurol 53:795-800, Boeve,B.F.,et al, 1999
Safety and Factors Related to Survival After Percutaneous Endoscopic Gastrostomy in ALS
Neurol 53:1123-1125, Chio,A.,et al, 1999
Brachial Amyotrophic Diplegia, A Slowly Progressive Motor Neuron Disorder
Neurol 53:1071-1076, Katz,J.S.,et al, 1999
An Algorithm for ALS Diagnosis and Management
Neurol 53:S58-S62, Swash,M., 1999
MR Findings in AIDS-Associated Myelopathy
AJNR 20:1412-1416,1387, Chong,J.,et al, 1999
Attitudes of Patients with Amyotrophic Lateral Sclerosis and Their Care Givers Toward Assisted Suicide
NEJM 339:967-973,987, Ganzini,L.,et al, 1998
Olfactory Dysfunction in Guamanian ALS,Parkinsonism,and Dementia
Neurol 51:1672-1677, Ahlskog,J.E.,et al, 1998
Amyloid Neuropathy Simulating Lower Motor Neuron Disease
Neurol 51:600-602, Quattrini,A.,et al, 1998
Consequences of the Delayed Diagnosis of Ataxia-Telangiectasia
Pediatrics 102:98-100, Cabana,M.D.,et al, 1998
Poliomyelitis-Like Illness Due to Japanese Encephalitis Virus
lancet 351:1094-1097, Solomon,T.,et al, 1998
An Analysis of Extended Survival in Patients with Amyotrophic Lateral Sclerosis Treated with Riluzole
Arch Neurol 55:526-528, Riviere,M.,et al, 1998
Sleep Apnea in Patients with Postpolio Syndrome
Ann Neurol 43:661-664, Dean,A.C.,et al, 1998
Magnetic Resonance Imaging of Muscle in Amyotrophic Lateral Sclerosis
Neurol 51:110-113, Bryan,W.W.,et al, 1998
Progressive Atrophy of Cerebellum & Brainstem, Age & Size of Expanded CAG Repeats in the MJDI Gene in Machado-Joseph Dis
Ann Neurol 43:288-296, Onokera,O.,et al, 1998
Steroid-Responsive Myopathy with Deficient Chondroitin Sulfate C in Skeletal Muscle Conn Tissue
Neurol 50:526-529, Al-Lozi,M.T.,et al, 1998
MR Findings of Werdnig-Hoffmann Disease in Two Infants
AJNR 19:550-552, Hsu,C.,et al, 1998
Distal Hereditary Upper Limb Muscular Atrophy
JNNP 64:217-220, Gross,D.W.,et al, 1998
Estimation of Brainstem Neuronal Loss in ALS with in Vivo Proton Magnetic Resonance Spectroscopy
Neurol 50:72-77, Cwik,V.A.,et al, 1998
Risk of Amyotrophic Lateral Sclerosis & History of Physical Activity, A Population Study
Arch Neurol 55:201-206, Longstreth,W.T.,et al, 1998
Toward Earlier Diagnosis of Amyotrophic Lateral Sclerosis, Revised Criteria
Neurol 50:768-772, Ross,M.A.,et al, 1998
Flail Arm Syndrome: A Distinctive Variant of Amyotrophic Lateral Sclerosis
JNNP 65:950-951, Hu, M.T.M.,et al, 1998
An Infant with Encephalitis
Lancet 350:1594, Yeung,W.L.,et al, 1997
Frontotemporal Degeneration, Pick Disease, and Corticobasal Degeneration
Arch Neurol 54:1425-1427, 14291997., Neary,D., 1997
Frontotemporal Dementia, Pick Disease, and Corticobasal Degeneration
Arch Neurol 54:1427-1429, Kertesz,A., 1997
Cerebral & Cerebellar Atrophy on Serial MRI in an Initially Symptom Free Subject at Risk of Familial Prion Disease
BMJ 315:856-857, Fox,N.C.,et al, 1997