Cogan Syndrome An Analysis of Reported Neurological Manifestations
The Neurologist 18:55-63, Antonios,N. and Silliman,S., 2012
Acute Leukoencephalopathies:Differential Diagnosis and Investigation
The Neurologist 4:148-166, Weinshenker,B.G.,et al, 1998
A 66-Year-Old Woman With Progressive Encephalopathy and Bilateral Hearing Loss
Neurol 100:254-258, Rivers,D.,et al, 2023
A 24-Year-Old Pregnant Woman with Headache and Behavioral Change Progressing to Coma
Neurol 101:e2331-e2337, Barnardes,C.,et al, 2023
A 72-Year-Old Woman with Rapidly Progressive Bilateral Hearing Loss
Neurol 98:632-637, Alsalem, A.,et al, 2022
A 42-Year-Old Woman with Mysterious Monocytic Meningitis
Neurol 97:449-454, Nothem, M.E., et al, 2021
Chronic Meningitis
NEJM 385:930-936, Aksamit, A.J., 2021
Spontaneous Intracranial Hypotension
NEJM 385:2173-2178, Schievink, W.I., 2021
Neurobrucellosis Brief Review
Neurologist 26:248-252, Bouferraa,Y.,et al, 2021
Case Report: Anti-NMDA Receptor Encephalitis with Bilateral Hearing Loss as the Initial Symptom
Front Neurol doi:10.3389/FNEUR.2021.648911, Cheng,H.,et al, 2021
Migraine, hearing loss, and blurred vision in a young woman
Neurol 95:e2945-e2950, Sasikumar, S.,et al, 2020
A Woman in her 40s with Transient Neurological Symptoms, Migraine Headaches, and Hearing Loss
JAMA Neurol 76:504-505, Roshal, D.A.,et al, 2019
Clinicopathologic Conference, Susacs Syndrome
NEJM 379:2152-2159, Case 37-2018, 2018
Clinicopathologic Conference, MELAS (mitochondrial encephalopathy, lactic acidosis, and stroke like episodes)
NEJM 376:1668-1678, CASE 13-2017, 2017
Snowball-like Lesions with Sudden Hearing Loss
Neurol 82:e100, Oliveira, P. & Mayeux, J., 2014
Acoustic Apoplexy: An Acute Complication of a Common Intracranial Tumour
BMJ 348:g3268, Hollingworth, M.A.,et al, 2014
Teaching NeuroImages: A Case of Hearing Loss in a Paraneoplastic Syndrome Associated with Anti-Hu Antibody
Neurol 79:e134, Renna, R.,et al, 2012
Acute Unilateral Hearing Loss as an Early Symptom of Lateral Cerebral Sinus Venous Thrombosis
Arch Neurol 69:1508-1511, Gattringer, T.,et al, 2012
Clinicopathologic Conference, Susacs Syndrome (retinocochleocerebral vasculopathy)
NEJM 365:549-559, Case 24-2011, 2011
Neurofibromatosis Type 2
Lancet 373:1974-1986, Astagiri,A.R.,et al, 2009
A 28-Year-Old Pregnant Woman with Encephalopathy
Neurol 73:e74-e79, Grinspan,Z.,et al, 2009
Clinical Features: Outcome, and Meningococcal Genotype in 258 Adults With Meningococcal Meningitis: A Prospective Cohort Study
Medicine 87:185-192, Heckenberg,S.G.B.,et al., 2008
Causative Factors and Epidemiology of Bilateral Vestibulopathy in 255 Patients
Ann Neurol 61:524-532, Zingler,V.C.,et al, 2007
Update on Susacs Syndrome
Curr Opin Neurol 18:311-314, Gross,M. &Eliashar,R., 2005
Susac Syndrome:Report of Four Cases and Review of the Literature
AJNR 25:382-388,351, Do,T.H.,et al, 2004
Neurobrucellosis:Clinical and Neuroimaging Correlation
AJNR 25:395-401, Al-Sous,M.W.,et al, 2004
Neurologic Manifestations in Primary Sjogren Syndrome: A Study of 82 Patients
Medicine 83:280-291, Delalande,S.,et al, 2004
MRI Findings in Susac's Syndrome
Neurol 61:1783-1787, Susac,J.O.,et al, 2003
Sudden Sensorineural Hearing Loss Associated with Herpes Simplex Virus Type 1 Infection
Neurol 56:571-572, Rabinstein,A.,et al, 2001
Acute Bilateral Sensorineural Hearing Loss as the Presenting Symptom of Metastatic Lung Cancer
Otolaryngol Head Neck Surg 124:592-594, Snyder, M.C. & Heywood, B., 2001
Meningeal Carcinomatosis Manifested as Bilateral Progressive Sensorineural Hearing Loss
Am J Otol 21:510-512, Shen,T.Y., &Young,Y.H., 2000
Superficial Siderosis of the Central Nervous System,A Late Complication of Cerebellar Tumors
Neurol 52:163-169, Anderson,N.E.,et al, 1999
Retinocochleocerebral Vasculopathy
Medicine 77:12-40, Petty,G.W.,et al, 1998
Susac Syndrome
Medicine 77:3-11, Papo,T.,et al, 1998
Acute Vestibular Syndrome
NEJM 339:680-685, Hotson,J.R.&Baloh,R.W., 1998
Neurologic Aspects of Inflammatory Bowel Disease
Neurol 45:416-421, Lossos,A.,et al, 1995
Susac's Syndrome:Triad of Microangiopathy of the Brain and Retina with Hearing Loss in Young Women
Neurol 44:591-593, Susac,J.O., 1994
Clinicopath Conf
Primary Malignant Lymphoma of CNS, Diffuse, Large-Cell]B-Cell Type, Case 36-1994, NEJM 331:861-8684., , 1994
TORCH Infections in the Newborn
Semin Neurol 13:106-115, Donley,D.K., 1993
MR Imaging of the Spinal Cord in 23 Subjects with ALD-AMN Complex
AJR 158:413-416, Snyder,R.D.,et al, 1992
Small Infarctions of Cochlear, Retinal, and Encephalic Tissue in Young Women
Stroke 23:903-907, Schwitter,J.,et al, 1992
Microangiopathy of the Brain, Retina, and Ear:Improvement without Immunosuppressive Therapy
Stroke 22:933-937, Gordon,D.L.,et al, 1991
Chronic Neurologic Manifestations of Lyme Disease
NEJM 323:1438-1444, Logigian,E.L.,et al, 1990
Neurobrucellosis:Clinical Characteristics, Diagnosis, and Outcome
Neurol 39:498-501, AlDeeb,S.M.,et al, 1989
Neurofibromatosis 2 (Bilateral Acoustic Neuro-fibromatosis)
NEJM 318:684-688, Martuza,R.L.&Eldridge,R., 1988
A Microangiopathic Syndrome of Encephalopathy, Hearing Loss & Retinal Arteriolar Occlusions
Neurol 35:1113-1121, Monteiro,M.L.R.,et al, 1985
Niemann-Pick Type C Disease
www.UpToDate.com, Nov, Schiffmann, R., 2026
Bilateral Posterior Limb Internal Capsule T2 Hyperintensity and Severe Cerebellar Atrophy in 2 Lifelong Friends
Neurol 106:e218014, Inoue,H.,et al, 2026
Melas Syndrome
Stat PearlsPubl Jan 25, Pia,S. & Lui,F., 2025