A 49-Year-Old Man with Meningoencephalitis and Persistent Altered Mental Status
Neurol 106:e214777, Hariswar,P.T.,et al, 2026
Niemann-Pick Disease Type C
Gene Reviews www.genereview.org, Bremova-Ertl,T. & Patterson, M., 2025
Rapidly Progressive Thalamic Dementia
Neurol 96:e809-e813, Rizzo, A.C.,et al, 2021
Clinicopathologic Conference, Normal Pressure Hydrocephalus
NEJM 384:1350-1358, Case 10-2021, 2021
Neuropathy, Encephalopathy, Status Epilepticus, and Acute Intermittent Porphyria
Lancet 395:e101, Ahmed, M.A.,et al, 2020
Clinicopathologic conference, Frontotemporal Lobar Degeneration with tau-positive inclusions consistent with Picks disease
NEJM 383:2666-2675, Case 41-2020, 2020
Acute Encephalitis in Immunocompetent Adults
Lancet 393:702-716, Venkatesan, A.,et al, 2019
Childhood Primary Angiitis of the Central Nervous System
www.UptoDate.com, Dec, Twilt, M. & Benseler, S., 2019
Teaching NeuroImages: Acute Necrotizing Encephalopathy of Childhood
Neurol 90:e177-e178, Biswas, A.,et al, 2018
A 54-year-old woman with Confusion and Visual Disturbances
Neurol 91:363-367, Rossi, K.C.,et al, 2018
Clnicopathologic Conference Anti-N-Methyl-D-Aspartate (NMDA) Receptor Encephalitis
NEJM 379:870-878, CASE 27-2018, 2018
Pyruvate Dehydrogenase Deficiency (PDCD)
eMedicine.medscape,com, Aug, Frye,R.E.,et al, 2018
Investigations in GABA? Receptor Antibody-Associated Encephalitis
Neurol 88:1012-1020,1010, Spatola, M.,et al, 2017
Precipitous Deterioration of Motor Function, Cognition, and Behavior
JAMA Neurol 74:591-596, Fernandez-Fournier, M.,et al, 2017
Huntington Disease: Clinical Features and Diagnosis
UptoDate Dec 2017, Oksana Suchowersky, 2017
Clinicopathologic Conference, Neurosarcoidosis
NEJM 374:1966-1975, Case 15-2016, 2016
A Young Man with Progressive Language Difficulty and Early-Onset Dementia
JAMA Neurol 73:595-599, Botha, H.,et al, 2016
Clinicopathologic Conference, Frontotemporal Lobar Degeneration with Tau-positive Inclusions (Picks Disease Subtype) Due to a Gly389Arg MAPT Mutation, Resulting in the Behavioral Variant of Frontotemporal Dementia with Parkinsonism
NEJM 372:1151-1162, Miller, B.L.,et al, 2015
Molybdenum Cofactor Deficiency
Neurol 85:e175-e178, Nagappa, M.,et al, 2015
Hippocampal Sclerosis after Febrile Status Epilepticus: The FEBSTAT Study
Ann Neurol 75:178-185,173, Lewis, D.V.,et al, 2014
Actionable Diagnosis of Neuroleptospirosis by Next-Generation Sequencing
NEJM 370:Doi:10.1056/NEJMoal1401268, Wilson, M.R.,et al, 2014
Effect of Rituximab in Patients with Leucine-Rich, Glioma-Inactivated 1 Antibody-Associated Encephalopathy
JAMA Neurol 71:896-900, Irani, S.R.,et al, 2014
Neuroimaging Features and Predictors of Outcome in Eclamptic Encephalopathy: A Prospective Observational Study
AJNR 35:1728-1734, Junewar, V.,et al, 2014
Inherited Metabolic Diseases of the Nervous System, Subacute Necrotizing Encephalopathy (Leigh Disease)
Adams & Victors Principles of Neurology, Chp 37, pg 996, Ropper, A.H.,et al, 2014
Clinicopathologic Conference, Oligoastrocytoma, Grade II with Temporal-Lobe Seizure and Ictal Asystole (Arrhythmogenic Epilepsy)
NEJM 368:2304-2312, Case 18-2013, 2013
Sturge-Weber Syndrome
MedLink Neurology, July, Comi, A.M., 2013
Febrile Infection-Related Epilepsy Syndrome: A Study of 12 Patients
Seizure 22:553-559, Caraballo, R.H.,et al, 2013
Autoimmune Epilepsy
Arch Neurol 69:582-593,565, Quek, A.M.L.,et al, 2012
MRI Abnormalities Follwing Febrile Status Epilepticus in Children
Neurol 79:871-877, Shinnar, S.,et al, 2012
MRI and EEG as long-term seizure outcome predictors in familial mesial temporal lobe epilepsy
Neurol 79:2349-2354, Morita, M.,et al, 2012
Presentation, Diagnosis, Pathophysiology, and Treatment of the Neurological Features of Sturge-Weber Syndrome
The Neurologist 17:179-184, Comi, A.M., 2011
Treatment of Severe Neurological Deficits with IgG Depletion through Immunoadsorption in Patients with Escherichia coli O104:H4-Associated Haemolytic Uraemic Syndrome: A Prospective Trial
Lancet 378:1166-1173,1120, Greinacher, A.,et al, 2011
Autoimmune Limbic Encephalitis with GAD Antibodies
The Neurohospitalist 1:178-181, Finelli, P.F., 2011
Prospective Study of New-Onset Seizures Presenting as Status Epilepticus in Childhood
Neurol 74:636-642, 624, Singh,R.K.,et al, 2010
New-Onset Refractory Status Epilepticus with Restricted DWI and Neuronophagia in the Pulvinar
Neurol 74:1003-1005, Boyd,J.G.,et al, 2010
Status Epilepticus Migrainosus: Clinical, Electrophysiologic, and Imaging Characteristics
Neurol 75:373-374, Perucca,P., et al, 2010
Sporadic Creutzfeldt-Jakob Disease Mimicking Nonconvulsive Status Epilepticus
Neurol 74:1995-1999, Lapergue,B., et al, 2010
Non-Paraneoplastic Limbic Encephalitis Characterized by Mesio-Temporal Seizures and Extratemporal Lesions: A Case Report
Seizure 19:446-449, Cianci,V.,et al, 2010
Brain Biopsy in Children With Primary Small-Vessel Central Nervous System Vasculitis
Ann Neurol 68:602-610, 573, Elbers,J.,et al, 2010
Acute Limbic Encephalitis and Glutamic Acid Decarboxylase Antibodies:A Reality?
J Neurosci 287:69-71, Blanc,F.,et al, 2009
Restricted Diffusion on Magnetic Resonance Imaging in Partial Status Epilepticus
Arch Neurol 65:278-279, Buracchio,T.,et al, 2008
Non-Paraneoplastic Limbic Encephalitis Associated with Anti-Glutamic Acid Decarboxylase Antibodies
J Neuroimmunol 199:155-159, Mata,S.,et al, 2008
Prognosis of Children With Partial Epilepsy: MRI and Serial 18FDG-Pet
Neurol 68:665-659, Gaillard,W.D.,et al, 2007
Epilepsy in Children
Lancet 367:499-524, Guerrini,R., 2006
The "Electrocuted" Hippocampus
Lancet 366:956-957, Uncini,A.,et al, 2005
Diffusion-weighted and Perfusion MRI Demonstrates Parenchymal Changes in Complex Partial Status Epilepticus
Brain 128:1369-1376, Szabo, K.,et al, 2005
Potentially Reversible Autoimmune Limbic ncephalitis with Neuronal Potassium Channel Antibody
Neurol 62:1177-1182,1040, Thieben,M.J.,et al, 2004
Clinical Spectrum of Succinic Semialdehyde Dehydrogenase Deficiency
Neurol 60:1413-1417, Pearl,P.L.,et al, 2003
MRI Changes in Status Epilepticus
Neurol 60:1866, Sirven,J.I.,et al, 2003